PityriasisLichenoidesChronica ( PLC ) Turning into Febrile UlceronecroticMucha - HabermannDisease : A Case Report
نویسنده
چکیده
PityriasisLichenoidesChronica(PLC) ,PityriasisLichenoides Et VarioliformisAcuta(PLEVA), Febrile UlceronecroticMucha-Habermann Disease(FUMHD) all represent clinicopathological spectrum of same disease entity. FUMHD is a rare febrile variant of PLEVA characterised by necrotic cutaneous ulcerations associated with high fever and systemic manifestations. Hereby we report a 11 year old male, who initially presented with lesions of PLC which healed with oral erythromycin for 8 weeks but in 3 months he again presented with generalised ulceronecrotic lesions on skin, continuous high grade fever and abdominal pain suggestive of Mucha-Habermann Syndrome. He responded only to systemic corticosteroids. Disease being a clinical spectrum, it is important to follow up the patients presenting with PLC and having a watchful suspicion as it can turn into potentially fatal MHD.
منابع مشابه
Is mycophenolate mofetil a new treatment for pityriasis lichenoides? A case report
Pityriasis lichenoides is an uncommon, acquired, papulosquamous disorder that exhibits various clinical presentations, including acute, chronic, and febrile ulceronecrotic Mucha- abermann forms. Pityriasis lichenoides chronica (PLC) is the chronic form of this continuum. Its treatment is challenging for patients and clinicians and some cases are multidrug resistant. Today, this disorder has man...
متن کاملPityriasis lichenoides chronica presenting with bilateral palmoplantar involvement.
Pityriasis lichenoides is an uncommon, acquired, idiopathic, self-limiting skin disease that poses a challenge to patients and clinicians to diagnose and treat. Several variants exist including pityriasis lichenoides et varioliformis acuta (PLEVA), pityriasis lichenoides chronica (PLC), and febrile ulcer-onecrotic Mucha-Habermann disease. Precise classification can be difficult due to an overla...
متن کاملCorrelation of Serum Zinc Level with Simple Febrile Seizures: A Hospital based Prospective Case Control Study
Background: Febrile seizures are one of the most common neurological conditions of childhood. It seems that zinc deficiency is associated with increased risk of febrile seizures.Aim: To estimate the serum Zinc level in children with simple Febrile seizures and to find the correlation between serum zinc level and simple Febrile seizures.Materials and Methods: The proposed study was a hospital ba...
متن کاملAutoimmune Encephalitis: A Case Presentation with Recurrent Febrile Seizures and Psychiatry Problems
Background: Autoimmune encephalitis is being diagnosed more and more often in the pediatric age group. It should be suspected in children with psychiatric symptoms, encephalopathy, abnormal movements or epileptic seizures. The most frequent autoimmune encephalitis in the pediatric is anti-N-methyl-D-aspartate (anti- NMDA) receptor encephalitis. Case report: We report a four-year-old boy with e...
متن کاملAtypical Kawasaki Disease Presenting with Hemiparesis and Aphasia: A Case Report
Kawasaki disease (KD) is an inflammatory vasculitis. KD is classified into two groups based on clinical characteristics criteria, namely classic and incomplete. Cerebral vascular abnormality, especially arterial ischemic stroke (AIS) is very rare and unusual in KD. Here, we report a 4-year-old boy who was referred to our tertiary pediatric center with abrupt right hemiparesis and aphasia. At ad...
متن کامل